rare!Newborn's hands and feet skin defects, carefully care for 25 days to make the "Butterfly Baby" grow skin

Wuhan Evening News, June 30th, was born, and Xiao Liuyi was found to be completely defective of the skin of both feet and palms. The bright red muscles were exposed, and it looked shocking. That night, he was transferred to Wuhan First Hospital for treatment. Faced with this rare congenital skin development, after 25 days of careful treatment and care, medical staff successfully helped the "Butterfly Baby" Xiao Liu 1 grow new skin. On June 25, Xiao Liuyi went home.

Before discharged, Mr. Guo and Ms. Ye took a photo with Xiao Liuyi and the medical staff, thanking them for letting the children recover their health so soon.

At 10 am on June 30, Ms. Ye and Mr. Guo in Huangpi held their son Xiao Liuyi at the door of the neonatal ward of Wuhan First Hospital. Xiao Liu was constantly twisted in his father's arms. "It's hot!" Mr. Guo shook his arms gently, coaxing gently in his mouth, and the little guy quickly calmed down.

This is the third time that Xiao Liuyi went to the hospital for the third time to change the medicine. The nurse gently unbuttoned the gauze wrapped in his left hand. The baby's palm only had one small nail cover the size of the skin lesions. After less than 5 minutes, the nurse changed the medicine. "Come again after 3 days! It is estimated that the medicine can be completely growing again!" Listening to the nurse's words, the eyes of the couple were a little moist. They know that this means that the son can be the same as normal children at this stage.

The baby is born with no skin and the skin of the limbs

On June 1st, for Ms. Ye and Mr. Guo, the young couple, as if they were on the "roller coaster" of life.

On this day, Ms. Ye, 29, ushered in the happiest moment in her life: as a mother. She couldn't wait to look at her child when she had a cesarean section. As a result, she almost fainted: the baby's hands and feet have no skin, the blood -red muscles are exposed, the blood vessels are clearly visible. Touching will rupture and bleed, facing the risk of infection at any time. The couple did not figure out that the baby was born with a full moon, and all inspections during pregnancy were green lights, and no one had ever had this situation in the two families!

The left hand with the worst skin defects of Xiao Liuyi has no skin at all, and there is pus in it.

The medical staff present have never seen this. The child's condition is very critical! Huangpi District Maternal and Child Health Hospital immediately contacted Wang Na, Director of the Freshman Department of Wuhan First Hospital. After receiving the call, Wang Na immediately opened a newborn to treat the green channel and sent a special ambulance for transport.

The ambulance galloped all the way. After arriving at Wuhan First Hospital at 0:30 in the morning, Xiao Liuyi was sent to the neonatal intensive care unit.

A rare disease with a incidence of 100,000 in the incidence

At 8 o'clock in the morning, Wang Na invited the dermatologist to clinic. Xiao Liuyi's hands and feet skin defects look like "congenital skin development." This is a rare genetic disease, with a incidence of about 100,000, and the literature shows that the mortality rate is about 17.8%. As soon as the child was born, irregular skin defects appeared, like ulcer surfaces, and the surface covered with a thin, transparent, and fragile membrane structure. The depth of the defect was different. Only hundreds of cases were reported around the world.

To confirm the diagnosis, genetic testing must be done. Take a sample of the skin tissue for the baby and send it to the relevant institutions of Xiamen to test it. At the same time, the child's skin lesions are sent to Beijing. Soon, experts gave diagnosis opinions: high suspected congenital skin development. At present, there is no good treatment at home and abroad for this disease, which can only be treated symptomatically.

The feet are only covered with a thin layer of film.

The defective skin of Xiao Liuyi is still having blistering, the tissue liquid seeps out, and the fingers are full of pus. "This is the first time that our neonatal chronic care unit was cured after the opening of the department." Wang Na said that rare diseases are first of all diagnosis. Now they can basically clarify the diagnosis. The biggest challenge is nursing. Epidermal defects are very easy to cause infection. Once infected, it will cause sepsis to life. The key to the treatment of "Baby Butterfly" is wound treatment, to prevent infection, promote wound healing as soon as possible, and regenerate skin.

The newborn department is equipped with a special personnel for Xiao Liuyi, and also set up a nursing team for him. Yang Chunxue, the head of the nurses of various types of wound wounds, led Xu Ting and other nursing backbones. Nursing plan.

Spend 25 days to help Xiao Liuyi repair the "armor"

Xiaoliu's skin lesion area accounts for 8%of the skin's skin area, and each change of medication is a painful torture for the baby.

The medical staff looked in their eyes and pain in their hearts. Every time they change the medicine, they will prepare a pacifier and oral glucose for the baby in advance. When changing the medicine, one group of nurses, one holding him to soothe him, one responsible for fixing the affected limb that needs to be changed, the other is the other, and the other is the other. Responsible for changing medicine. In the process of changing the medicine, they unveiled the dressing little by little, disinfected the wound with vitality iodine, then rinsed slowly with physiological saline, and then applied the drugs after drying. In order not to affect the baby's joint activity, they cut the dressing into small pieces, and the fingers and toe joints were separated and fixed to avoid the adhesion of the skin tissue affecting its function. Every time they change the medicine, they dare not produce at the atmosphere. They are found in 2 hours and have to be replaced twice a day.

Under the careful care of the medical staff, new skin quickly grew her small feet.

"Traditional concepts believe that the wound should be kept dry, so that this dry environment is not applicable to special skin problems such as butterfly babies." Yang Chunxue said that the wound is a dry environment, and the gauze is torn off. When it is adhesive, the wound will not only make the child feel pain, but also may damage the newly generated skin tissue and delay wound healing. The left hand with the worst skin defect is almost healed.

On the contrary, the wet environment is conducive to the dissolution of fibrin and necrotic tissues. It can also create a low oxygen environment, promote capillaries, promote the release of various growth factors and activate activity, and accelerate wound healing. Observation found that the technical care method of wet -nature replacement of Xiaoliuyi has not only eased the baby's wound pain, but also eliminates the invasion of bacteria from defective skin, reducing scar hyperplasia after healing.

Under the careful treatment and care of the medical staff, Xiao Liu was not infected throughout the whole process, and the skin damage wound "fighting" with pink new skin. On June 13, Xiao Liuyi turned to the maternal and baby ward. Seeing the right -handed and right foot skin that had completely returned to the normal son, Ms. Ye and Mr. Guo had been hanging a lot.

On June 25, the skin of Xiao Liuyi's left foot returned to normal, and the left hand with the most serious skin defects also had new skin in large areas.

(Reporter Liu Xuan intern Lin Xin'er correspondent Chen Cuiying Lingling Zhang Xinyu)

[Edit: Yu Lina]

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